Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy

[摘要] Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopathy, CMR revealed fibrosis in the lateral wall of the left ventricle. CMR is superior to conventional echocardiography for the detection of myocardial fibrosis in desmin-related cardiomyopathy, which may be useful to detect early cardiac involvement and predict the patient prognosis.

[发布日期] 2010-11-18

[关键词] Cardiomyopathy;Cardiovascular Magnetic Resonance;Late Gadolinium Enhancement;Brain Natriuretic Peptide;Myocardial Fibrosis