An incidental presentation of Herlyn–Werner-Wunderlich syndrome with secondary infertility: A case report

[摘要] Rationale:  Herlyn-Werner-Wunderlich syndrome, also known as obstructed hemi-vagina with ipsilateral renal agenesis (OHVIRA) syndrome, is a rare congenital anomaly of the Müllerian and Wolffian ducts. It is often asymptomatic until puberty and is usually misdiagnosed as infertility. Patient concerns:  A 39-year-old woman desirous of pregnancy was referred to our radiodiagnosis unit for imaging evaluation on account of secondary infertility. Diagnosis:  Incidental discovery of uterine bicornis bicollis and blind-ending hemivagina was noted at hysterosalpingography. Interventions:  This necessitated the search for other genitourinary tract anomalies, and ipsilateral renal agenesis was also discovered. Outcomes:  A diagnosis of Herlyn-Werner-Wunderlich syndrome was made. Lessons:  Magnetic resonance imaging (MRI) is considered the gold standard imaging modality for the assessment of uterine malformations. However, in resource-poor centers where MRI is unavailable, a heightened clinical suspicion with the combination of available imaging modalities is important and reliable in making an accurate diagnosis, hence, successful management.

[学科分类] 兽医学

[关键词] Infertility;Obstructed hemivagina;Renal agenesis;Uterus didelphys;Herlyn-Werner-Wunderlich syndrome