Agenesis of the Dorsal Pancreas

[摘要] Background: Agenesis of the dorsal pancreas (ADP) is a rare entity, which is often diagnosed incidentally on abdominal imaging. It can present with abdominal pain or with symptoms of exocrine and endocrine deficiency. Approximately half of patients with ADP will have a diagnosis of diabetes mellitus, and up to half of them will require insulin therapy. Case Report: Abdominal CT in a 39-year-old man with antibody negative type 1 diabetes and chronic abdominal pain revealed dorsal pancreatic agenesis without any focal pancreatic lesions or evidence of pancreatitis. An MRCP showed normal hepatobiliary anatomy. He was replete for fat soluble vitamins. Investigations at the time of diabetes diagnosis demonstrated relative insulin deficiency. Conclusion: The case highlights that ADP is a rare cause of abdominal pain, which is often diagnosed incidentally on abdominal imaging.

[学科分类] 生理学

[关键词] Abdominal Pain;Diabetes Mellitus;Insulin;Pancreas Agenesis;Vitamins.