VACTERL syndrome with late presentation of annular pancreas with duodenal web: Case report

[摘要] VACTERL Syndrome affects multiple body systems and can include various anomalies of the Vertebral column, Anus and/or rectum , heart (Cardiac), Tracheo-Esophagus, kidneys (Renal), and Limbs. Patients with VACTERL syndrome are at increased risk of having a congenital duodenal obstruction that may be extrinsic in the form of an annular pancreas or intrinsic in the form of duodenal atresia , stenosis or web. Simultaneous presentation of both the annular pancreas and duodenal web is a rare clinical entity and typically presents in neonates. However, late presentation of annular pancreas combined with a duodenal web is exceedingly uncommon. We present a case of late diagnosis of annular pancreas with duodenal web resulting in an entrapped ingested foreign body.

[学科分类] 生物化学工程

[关键词] Annular pancreas;Duodenal web;VACTERL Syndrome;Foreign body