A Case of Ovarian Fibromatosis and Massive Ovarian Oedema Associated With Intra-Abdominal Fibromatosis, Sclerosing Peritonitis and Meig's Syndrome

[摘要] Purpose:To discuss a case of ovarian fibromatosis/massive ovarian oedema, intra-abdominal fibromatosis, sclerosingperitonitis and Meig's syndrome. To review the reported therapeutic options.Patients:Case report of a 27-year-old female with the combined pathology of ovarian fibromatosis/massive ovarian oedema,intra-abdominal fibromatosis, sclerosing peritonitis and Meig's syndrome.Methods:This patient was treated with supportive care and cytotoxic chemotherapy.Results:Despite the benign nature of the ovarian pathology, this patient presented with life-threatening complications.Response to treatment was probably multi-factorial combining the effects of cytotoxics, use of steroids and good supportivecare. She remains in complete remission 4 years post completion of chemotherapy.Conclusion:There are reports in the literature of ovarian fibromatosis/massive ovarian oedema, luteinised thecomas, intraabdominalfibromatosis and Meig's syndrome occurring together in a variety of combinations. Treatment has been describedwith radiotherapy, cytotoxic and non-cytotoxic chemotherapy regimens. This case provides a link between ovarianfibromatosis/massive ovarian oedema, intra-abdominal fibromatosis, sclerosing peritonitis and Meig's syndrome notpreviously described.

[学科分类] 肿瘤学