Periosteal Ewing's Sarcoma: Report of Two New Cases and Review of the Literature

[摘要] Background.The origin of Ewing's sarcoma in a periosteal location israre and not clearly documented. Other malignant bone tumors appear to have a somewhat better prognosis when confined between periosteum and bone. Is it the same for periosteal Ewing's sarcoma?Methods.We describe two new cases and comprehensivelyreview the literature consisting of 18 documented cases since the condition was firstdescribed in 1986 (S.M. Bator.Cancer58:1781– 4).Results.Periosteal Ewing's sarcoma differs from the other formsof Ewing's sarcoma in terms of sex predominance, location of tumor, surgical stage atpresentation and typical imaging studies. Eighteen out of the 20 patients werereported to be alive with no evidence of disease.Conclusions.It seems that the prognosis of this rare variant ofEwing's sarcoma family of tumors might be better but the small number of casesprecludes such a firm conclusion.

[学科分类] 肿瘤学