Two Egyptian cases of lipoid proteinosis successfully treated with acitretin

[摘要] Lipoid proteinosis (Urbach-Wiethe disease) is a rare progressive autosomal recessive disorder, characterized histologically by deposition of periodic acid Schiff-positive, diastase resistant, hyaline-like material into the skin, upper aerodigestive tract, and internal organs.

[学科分类] 皮肤病学

[关键词] acitretin;blister;genodermatoses;hoarseness;lipoid proteinosis;pharynx;throat