ASSOCIATION OF TRANSPOSITION OF THE GREAT VESSELS AND RUDIMENTARY RIGHT VENTRICLE, WITH AND WITHOUT TRICUSPID ATRESIA

[摘要] A group of eight cases with three different combinations of congenital cardiac defects but similar clinical findings has been presented. The differential diagnosis from other types of congenital heart disease has been discussed. All had transposition of the great vessels and same obstruction to aortic outflow, either subaortic stenosis or a rudimentary right ventricle from which the aorta arose. Six cases had tricuspid atresia and two had rudimentary right ventricle without tricuspid atresia.The salient features were:1) Early congestive failure.2) Absent or minimal cyanosis.3) Large heart and pulmonary congestion roentgenographically.4) Electrocardiographic findings of peaked P waves and a pattern of left ventricular hypertrophy.5) Angiocardiographic findings of a right to left atrial shunt, failure to visualize the right ventricle, early opacification of the left ventricle and pulmonary artery, and late and inadequate opacification of a small aorta.

[学科分类] 儿科学