The TailgutCyst is an embryological remnant of the hindgut that can be a part of theCurrarino Syndrome. Report of a case: A 43-year-old woman with lombalgy, urineretain and presacral mass. Preceding history of ectopic anus, constipation associatedwith congenital megacolon. Imaging exams indicate retrorectal cyst that compressesthe sacral region, receding the pelvic structure forward and congenital sacraldeformity. A block resection of the retrorectal, rectal, uterus and sacrum lesionwas carried out in a S2 level. Anatomo-pathologic indicate tailgut cyst.The patient is characterized as carrying the Currarino Syndrome. Discussion:The syndrome is characterized by the malformation of the anorectal, sacral abnormaltiesand retrorectal mass. It has connection with a gene mutation of the HLXB9. TheTailgut Cyst is an embryological remnant of the hindgut, more commonin young adult women (75-90%). The tailgut cyst related to the CurrarinoSyndrome is an uncommom lesion. Most patients are asymptomatic, however, theymay present anorectal, perineo and sacrum symptoms. Imaging exams are usefulfor diagnostic definition and surgery programming. The complete surgery excisionis recommended due to the risk of reestablishment, malignant degeneration andchronic infection, even in asymptomatic patients. The prognosis is uncertain.
