Carney’s Triad

[摘要] Background: Carney triad (gastric leiomyosarcoma, pulmonary chondroma and extra-adrenal paraganglioma) is a rare syndrome comprising of multiple tumors of unknown etiology.  Long-term follow-up shows that the syndrome is chronic and generally indolent and persistent; outcome is largely dependent on the behaviour of the metastases of the gastric sarcoma. Case Report: We report a case of 16-year-old girl who presented with full triad (multiple bilateral pulmonary chondroma and adrenal tumor) and was treated with surgery for gastric GIST and adjuvant imatinib. Conclusion: This report will sensitize the physicians about the possibility of Carneys triad, especially in young females presenting with one of the three components at unusual locations.

[学科分类] 生理学

[关键词] Home page Right