Arrhythmogenic Right Ventricular Cardiomyopathy or Dilated Cardiomyopathy associated with Partial Hypopituitarism

[摘要] Background: Arrhythmogenic right ventricular cardiomyopathy (ARVC), also known as arrhythmogenic right ventricular dysplasia, is a heritable heart-muscle disorder that predominantly affects the right ventricle. Progressive loss of right ventricular myocardium and its replacement by fibrofatty tissue is the pathological hallmark of the disease. Case Report: A 25-year-old female presented with dyspnea from last one year. Her symptoms included fatigue, weakness, inability to lose weight, puffiness, and constipation.  Echocardiogram and cardiac MRI were consistent with diagnostic criteria of ARVC formulated in 2010 by the revisited Task Force, with two major or one major and two minor criteria or four minor criteria. Conclusion: Cardiac magnetic resonance (MRI) is considered the best imaging modality in evaluating the RV in ARVC.

[学科分类] 生理学

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