Surgical management of pygopagus conjoined twins with spinal bifida

[摘要] PurposeConjoined twins are a rare complication of 9 monozygotic twins and are associated with high perinatal mortality. Pygopagus are one of the rare types of conjoined twins with only a handful of cases reported in the literature.Case summaryWe present the case of one-and-half month-old male pygopagus conjoined twins, who were joined together dorsally in lower lumbar and sacral region and had spina bifida and shared a single thecal sac with combined weight of 6.14 kg. Spinal cord was separated at the level of the conus followed by duraplasty. They had uneventful recovery with normal 15 months follow-up.ConclusionSeparation of conjoined twins is recommended in where this is feasible with the anticipated survival of both or one infant...

[学科分类] 骨科学

[关键词] Pygopagus ;Conjoined twins ;Separation surgery