Increased Vigilance Needed for the Detection of Thrombotic Complications of Central Venous Access in Adolescent Cystic Fibrosis Patients

[摘要] A 16-year-old Caucasian female CT (ΔF508/ΔF508) patient with pancreatic insufficiency and CF-related diabetes mellitus presented to our unit 2 years post-right-sided chest Port-A-Cath (indwelling CVC) insertion. She had developed acute hemoptysis and epistaxis with associated pleuritic chest pains. On auscultation of her chest, air entry was equal with no localized crepitations. Her pulmonary function tests revealed an FEV1 of 0.58 (23%) and an FEF of 25–75.17 (7%). These measurements were reasonably close to her baseline. A chest X-Ray revealed no evidence of pneumothorax. Her full blood count and coagulation screen were normal. Her symptoms resolved spontaneously and she was discharged.

[学科分类] 儿科学

[关键词] cystic fibrosis;thrombotic;thromboembolic;totally implantable venous access device;Port-A-Cath;indwelling venous catheter