A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature

[摘要] We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function.

[学科分类] 儿科学

[关键词] hepatorenal fibrocystic diseases;hepatoblastoma;autosomal recessive polycystic kidney disease;congenital hepatic fibrosis;Caroli syndrome